This A-Z list and basic information about each recognized autoimmune disease were compiled and written by our dedicated research team at the Global Autoimmune Institute. The list provides a starting point in learning about autoimmune diseases and immune-mediated conditions, with links to other sources that we believe to be accurate and informative. This section will be updated periodically.
*autoimmune-related or suspected autoimmune condition
| variant or subtype
/ synonym
*Anti-NMDA receptor encephalitis
Autoimmune Addison’s disease (AAD)
Autoimmune encephalitis | acute disseminated encephalomyelitis (ADEM)
Autoimmune hemolytic anemia (AIHA)
*Autoimmune hypophysitis/lymphocytic hypophysitis
*Autoimmune inner ear disease (AIED)
*Autoimmune lymphoproliferative syndrome (ALPS)
Autoimmune polyglandular syndromes, types I, II, & III (APS type 1, APS type 2, APS type 3, APECED)
Autoimmune progesterone dermatitis
*Autoimmune sudden sensorineural hearing loss (SNHL)
B*Birdshot chorioretinopathy / birdshot uveitis
CChronic inflammatory demyelinating polyneuropathy (CIDP)
Churg-Strauss syndrome / eosinophilic granulomatosis with polyangiitis (EGPA)
CREST syndrome | limited cutaneous systemic sclerosis
*Cronkhite-Canada syndrome (CSS)
*Cryptogenic organizing pneumonia (COP)
D*Dressler’s syndrome / postmyocardial infarction / postpericardiotomy syndrome
E*Eosinophilic esophagitis
*Essential mixed cryoglobulinemia
F*Fibrosing alveolitis/Idiopathic pulmonary fibrosis (IPF)
G*Giant cell arteritis / temporal arteritis / Horton’s disease
*Giant Cell Myocarditis
Goodpasture’s syndrome / anti-GBM/anti-TBM disease
Granulomatosis with polyangiitis (GPA) / Wegener’s granulomatosis
Graves disease / thyroid eye disease
HHashimoto’s thyroiditis / chronic lymphocytic thyroiditis / autoimmune thyroiditis
Henoch-Schönlein purpura / IgA vasculitis
Hurst’s disease / acute hemorrhagic leukoencephalitis (AHLE)
IIgA nephropathy / Berger's disease
*Immune-mediated necrotizing myopathy (IMNM)
Immune thrombocytopenia (ITP) / autoimmune thrombocytopenic purpura / autoimmune thrombocytopenia
*IgG4-related sclerosing disease (ISD)
JJuvenile idiopathic arthritis / Adult-onset Still's disease
*Juvenile polymyositis | Juvenile dermatomyositis | juvenile myositis
K*Kawasaki disease
LLambert-Eaton myasthenic syndrome (LEMS)
*Leukocytoclastic vasculitis
*Lichen planus | Lichen planopilaris
*Ligneous conjunctivitis
Linear IgA disease (LAD) | linear IgA bullous dermatosis (LABD)
*Lyme disease / chronic Lyme disease / post-treatment Lyme disease syndrome (PTLDS)
*Lymphocytic colitis/microscopic colitis
Lymphocytic hypophystitis/autoimmune hypophystitis
M*Microscopic polyangiitis (MPA)/ANCA-associated vasculitis
Mixed connective tissue disease (MCTD)
*Mooren’s ulcer
*Mucha-Habermann disease
*Multifocal motor neuropathy
*Myalgic encephalomyelitis (ME)/ Chronic fatigue syndrome (CFS)
N*Narcolepsy
Neuromyelitis Optica/Devic's disease
O*Opsoclonus-myoclonus syndrome (OMS)
PParaneoplastic cerebellar degeneration
*Parry-Romberg syndrome (PRS)/Hemifacial atrophy (HFA)/Progressive facial hemiatrophy
Paroxysmal nocturnal hemoglobinuria (PNH)
*Peripheral uveitis/pars planitis
*PANS/PANDAS
Pemphigus gestationis / herpes gestationis
*Pernicious anemia
*Postural orthostatic tachycardia syndrome (POTS)
Primary biliary cirrhosis (PBC) / primary biliary cholangitis
*Primary sclerosing cholangitis (PSC)
*Pulmonary fibrosis, idiopathic (IPF)
*Pyoderma gangrenosum
R*Rasmussen's encephalitis
Reactive arthritis / Reiter’s syndrome
*Reflex sympathetic dystrophy syndrome (RSD) / Complex regional pain syndrome (CRPS)
*Restless leg syndrome (RLS) / Willis-Ekbom disease
SSchmidt syndrome / autoimmune polyendocrine syndrome type II
*Sclerosing Mesenteritis / Mesenteric Panniculitis
*Serpiginous choroidopathy
*Stiff person syndrome (SPS)
Small fiber sensory neuropathy
Systemic lupus erythematosus (SLE)
*Subacute bacterial endocarditis (SBE)
*Subacute cutaneous lupus
*Susac syndrome
*Sympathetic ophthalmia
T*Takayasu’s arteritis (vasculitis)
Testicular autoimmunity (vasculitis, orchitis)
*Tolosa-Hunt syndrome
*Transverse myelitis (TM)
*Tubulointerstitial nephritis uveitis syndrome (TINU)
UUndifferentiated connective tissue disease (UCTD)
*Uveitis | anterior/intermediate/posterior
V*Vasculitis
*VEXAS Syndrome
*Vogt-Koyanagi-Harada syndrome (VKH)