Autoimmune Disease List

This A-Z list and basic information about each recognized autoimmune disease were compiled and written by our dedicated research team at the Global Autoimmune Institute. The list provides a starting point in learning about autoimmune diseases and immune-mediated conditions, with links to other sources that we believe to be accurate and informative. This section will be updated periodically.

*autoimmune-related or suspected autoimmune condition
| variant or subtype
/ synonym

Search By Disease Name


Disease By Letter

A

*Acromegaly

Acquired aplastic anemia

Acquired hemophilia

Agammaglobulinemia, primary

Alopecia areata

Ankylosing spondylitis (AS)

Anti-NMDA receptor encephalitis

Antiphospholipid syndrome (APS) | catastrophic antiphospholipid syndrome (CAPS) / Asherson's syndrome

*Arteriosclerosis

Autoimmune Addison’s disease (AAD)

Autoimmune autonomic ganglionopathy (AAG) / autoimmune dysautonomia | autoimmune gastrointestinal dysmotility (AGID)

Autoimmune encephalitis | acute disseminated encephalomyelitis (ADEM)

Autoimmune gastritis

Autoimmune hemolytic anemia (AIHA)

Autoimmune hepatitis (AIH)

*Autoimmune hyperlipidemia

*Autoimmune hypophysitis

*Autoimmune inner ear disease (AIED)

*Autoimmune lymphoproliferative syndrome (ALPS)

*Autoimmune myelofibrosis

Autoimmune myocarditis

Autoimmune oophoritis

Autoimmune pancreatitis (AIP)

Autoimmune polyglandular syndromes, types I, II, & III (APS type 1, APS type 2, APS type 3, APECED)

Autoimmune progesterone dermatitis

*Autoimmune retinopathy (AIR)

*Autoimmune sudden sensorineural hearing loss (SNHL)

B

Balo disease

Behçet’s disease

*Birdshot chorioretinopathy / birdshot uveitis

Bullous pemphigoid

C

*Castleman disease

Celiac disease

*Chagas disease

Chronic inflammatory demyelinating polyneuropathy (CIDP)

*Chronic urticaria (CU)

Churg-Strauss syndrome / eosinophilic granulomatosis with polyangiitis (EGPA) 

Cogan’s syndrome

Cold agglutinin disease

CREST syndrome |  limited cutaneous systemic sclerosis

Crohn’s disease (CD)

*Cronkhite-Canada syndrome (CSS)

*Cryptogenic organizing pneumonia (COP)

D

Dermatitis herpetiformis

Dermatomyositis

Diabetes, type 1

Discoid lupus

*Dressler’s syndrome / postmyocardial infarction / postpericardiotomy syndrome

E

*Eczema/Atopic Dermatitis

*Endometriosis

*Eosinophilic esophagitis

Eosinophilic fasciitis

*Erythema nodosum

*Essential mixed cryoglobulinemia

Evans syndrome

F

*Fibrosing alveolitis/Idiopathic pulmonary fibrosis (IPF)

G

*Giant cell arteritis / temporal arteritis / Horton’s disease

*Giant Cell Myocarditis

Glomerulonephritis

Goodpasture’s syndrome / anti-GBM/anti-TBM disease

Granulomatosis with polyangiitis (GPA) / Wegener’s granulomatosis

Graves disease / thyroid eye disease

Guillain-Barré syndrome (GBS)

H

Hashimoto’s thyroiditis / chronic lymphocytic thyroiditis / autoimmune thyroiditis

Henoch-Schönlein purpura / IgA vasculitis

*Hidradenitis suppurativa

Hurst’s disease / acute hemorrhagic leukoencephalitis (AHLE)

*Hypogammaglobulinemia

I

IgA nephropathy / Berger's disease

Immune-mediated necrotizing myopathy (IMNM)

Immune thrombocytopenia (ITP) / autoimmune thrombocytopenic purpura / autoimmune thrombocytopenia

*Inclusion body myositis

*IgG4-related sclerosing disease (ISD)

*Interstitial cystitis

J

Juvenile idiopathic arthritis / Adult-onset Still's disease

Juvenile polymyositis | Juvenile dermatomyositis | juvenile myositis

K

*Kawasaki disease

L

Lambert-Eaton myasthenic syndrome (LEMS)

*Leukocytoclastic vasculitis

*Lichen planus

*Lichen sclerosus

*Ligneous conjunctivitis

Linear IgA disease (LAD) | linear IgA bullous dermatosis (LABD)

Lupus nephritis

*Lyme disease /  chronic Lyme disease / post-treatment Lyme disease syndrome (PTLDS)

*Lymphocytic colitis/microscopic colitis

M

Ménière’s disease

*Microscopic polyangiitis (MPA)/ANCA-associated vasculitis

Mixed connective tissue disease (MCTD)

*Mooren’s ulcer

*Mucha-Habermann disease

*Multifocal motor neuropathy

Multiple sclerosis (MS)

*Myalgic encephalomyelitis (ME)/ Chronic fatigue syndrome (CFS)

Myasthenia gravis (MG)

N

*Narcolepsy

Neuromyelitis Optica/Devic's disease

O

Ocular cicatricial pemphigoid

*Opsoclonus-myoclonus syndrome (OMS)

P

Palindromic rheumatism

Paraneoplastic cerebellar degeneration

Paraneoplastic pemphigus

*Parry-Romberg syndrome (PRS)/Hemifacial atrophy (HFA)/Progressive facial hemiatrophy

Paroxysmal nocturnal hemoglobinuria (PNH)

*Peripheral uveitis/pars planitis

*PANS/PANDAS

Parsonage-Turner syndrome

Pemphigus gestationis / herpes gestationis

Pemphigus foliaceus

Pemphigus vulgaris

*Pernicious anemia

POEMS syndrome

Polyarteritis nodosa

Polymyalgia rheumatica

Polymyositis

*Postural orthostatic tachycardia syndrome (POTS)

Primary biliary cirrhosis (PBC)  / primary biliary cholangitis

*Primary sclerosing cholangitis (PSC)

Psoriasis

Palmoplantar Pustulosis

Psoriatic arthritis

*Pulmonary fibrosis, idiopathic (IPF)

Pure red cell aplasia (PRCA)

*Pyoderma gangrenosum

R

Raynaud’s syndrome/phenomenon

Reactive arthritis / Reiter’s syndrome

*Reflex sympathetic dystrophy syndrome (RSD) / Complex regional pain syndrome (CRPS)

Relapsing polychondritis

*Restless leg syndrome (RLS) / Willis-Ekbom disease

Rheumatic fever

Rheumatoid arthritis

S

Sarcoidosis

Schmidt syndrome / autoimmune polyendocrine syndrome type II

*Scleritis

Scleroderma 

*Sclerosing Mesenteritis / Mesenteric Panniculitis

*Serpiginous choroidopathy

Sjögren’s syndrome

*Stiff person syndrome (SPS)

Small fiber sensory neuropathy

Systemic lupus erythematosus (SLE)

*Subacute bacterial endocarditis (SBE)

*Susac syndrome

*Sydenham's chorea

*Sympathetic ophthalmia

T

*Takayasu’s arteritis (vasculitis)

Testicular autoimmunity (vasculitis, orchitis)

*Tolosa-Hunt syndrome

*Transverse myelitis (TM)

*Tubulointerstitial nephritis uveitis syndrome (TINU)

U

Ulcerative colitis (UC)

Undifferentiated connective tissue disease (UCTD)

*Uveitis | anterior/intermediate/posterior

V

*Vasculitis

*VEXAS Syndrome

Vitiligo

*Vogt-Koyanagi-Harada syndrome (VKH)

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